Case report: A case report of optic nerve glioma in a 5-year-old African girl
Keywords:
Optic Nerve Glioma, Neurofibromatosis 1, Meningioma, ExophthalmosAbstract
Background: Optic nerve gliomas are rare tumors that constitute less than 5%
of all pediatric central nervous system tumors.
Case Presentation: We present the case of a 5-year-old girl with complaints of
progressive protrusion of the right eye and poor vision of 3 years duration who
was referred to the ophthalmologist. Ophthalmological evaluation of the right
eye revealed tearing, no perception of light, inferior dystopia, severe proptosis,
and a firm non-tender orbital mass palpable posterior to the eyeball. The cranial
CT-scan was suggestive of a right optic nerve glioma. Histology showed Optic
Glioma with extensive proliferation of meningothelial cells.
Conclusion: Optic gliomas can be associated with extensive proliferation of
meningothelial cells that can histologically mimic a meningioma. It is
important to be cautious about making a diagnosis of meningioma for tumors
in locations that are also characteristic of optic nerve gliomas especially in
appropriate clinical settings.
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